Wilkies syndrome, or superior mesenteric artery syndrome smas, is a rare clinical condition characterized by partial or complete duodenal obstruction 1, 2. Read more about symptoms, diagnosis, treatment, complications, causes and prognosis. A 29yearold female was transferred to our hospital for management of duodenal obstruction. Wilkie collins 18241889, english novelist, playwright, and author of short stories. Superior mesenteric artery sma syndrome also known as wilkies syndrome is a rare cause of upper gastrointestinal obstruction. Wilkies syndrome with duodenojejunal diverticulosis. Wilkie disease partial or complete block of the superior mesenteric artery.
The superior mesenteric artery syndrome also known as wilkie s syndrome or as arteriomesenteric obstruction of the duodenumis a rare condition of upper intestinal obstruction in which the third. Wilkies syndrome is also known as superior mesenteric artery syndrome, cast syndrome, mesenteric root syndrome and chronic duodenal ileus 2. Superior mesenteric artery syndrome smas, also known as wilkies syndrome, is an exceedingly rare condition concerning intestinal obstruction. Wilkies syndrome is a rare condition that results from an intestinal. Introduction superior mesenteric artery sma syndrome or aortomesenteric compass syndrome or wilkies disease 1, 2 is a relatively rare condition caused by a short treitzs ligament, or by an unusually low. Superior mesenteric artery sma syndrome or wilkie s syndrome is a rare but potentially life threatening gastrointestinal condition. This syndrome is a clinical phenomenon believed to be caused by compression of the third part of the duodenum between the. Supportive and medical treatment was initiated with close liaison. Superior mesenteric artery sma syndrome also known as wilkie syndrome is an acquired vascular compression disorder in which acute angulation of the superior mesenteric artery sma results in compression of the third part of the duodenum leading to obstruction of proximal bowel.
A syndrome that is characterised by multiple congenital abnormalities. Pdf wilkies syndrome or superior mesenteric artery syndrome. Association of gastrointestinal motility disorders agmd. Jun 14, 2018 superior mesenteric artery syndrome smas is a digestive condition that occurs when the duodenum the first part of the small intestine is compressed between two arteries the aorta and the superior mesenteric artery.
Superior mesenteric artery sma syndrome is a gastrovascular disorder in which the third and final portion of the duodenum is compressed between the abdominal aorta aa and the overlying superior mesenteric artery. Wilkies syndrome or superior mesenteric artery syndrome. Superior mesenteric artery sma syndrome is a rare acquired disorder in which acute angulation of sma causes compression of the third part of the duodenum between the sma and the aorta, leading to obstruction. Superior mesenteric artery syndrome or wilkie syndrome. Ultrasound imaging in diagnosis of superior mesenteric artery. Superior mesenteric artery sma syndrome, also named as wilkies syndrome ws, is a rare entity caused by the obstruction of 3rd. Apr 17, 2008 wilkies syndrome, a rare cause of intestinal obstruction, is related to anatomical and mechanical factors associated with the reduction of retroperitoneal fat padding. Pdf superior mesenteric artery sma syndrome known as wilkies. Wilkies syndrome, well known as superior mesenteric artery syndrome, is a rare but wellrecognized clinical entity causing upper abdominal symptoms. Herein, we presented a patient with wilkies syndrome and discussed the diagnostic difficulties and surgical treatment options.
Wilkie syndrome or superior mesenteric artery syndrome is a rare cause of duodenal. Symptoms vary based on severity, but can be severely debilitating. It is an acquired disorder in which acute angulation of the sma causes compression of the third part of the duodenum between the sma and the aorta. Superior mesenteric artery sma syndrome or wilkies syndrome is a rare but potentially life threatening gastrointestinal condition. Functionally, the sma supplies the distal duodenum, twothirds of the. Pdf wilkie syndrome, also referred as superior mesenteric artery syndrome, is an unusual cause of a proximal small bowel obstruction.
Sma syndrome is also known as wilkie s syndrome, cast syndrome, mesenteric root syndrome, chronic duodenal ileus and intermittent arteriomesenteric occlusion. Media in category superior mesenteric artery syndrome the following 5 files are in this category, out of 5 total. Superior mesenteric artery sma syndrome which is also known as wilkies syndrome, is a rare cause of upper gastrointestinal obstruction. Its manifestations are due to compression of the third portion of the duodenum between the aorta and the superior mesenteric artery. The postmortem computed tomography scan showed compression of the duodenum by. Superior mesenteric artery syndrome wikimedia commons. If you have problems viewing pdf files, download the latest version of adobe reader.
She has tried proton pump inhibitors, glutenfree diet and lactosefree diet without any improvement. This results in chronic, intermittent, or acute complete or partial duodenal obstruction. Sma syndrome is also known as wilkies syndrome, cast syndrome, mesenteric root syndrome, chronic duodenal ileus and intermittent arteriomesenteric occlusion. Wilkie syndrome or superior mesenteric artery syndrome is a rare cause of duodenal obstruction in pediatric and adult age groups.
Wilkie s syndrome, also commonly known as superior mesenteric artery sma syndrome, is an infrequent and rare cause of small bowel obstruction. Wilkie syndrome, also referred as superior mesenteric artery syndrome, is an unusual cause of a proximal small bowel obstruction. Superiormesentericarterysyndrome is an ill characterized gastricoutlet. Pdf wilkies syndrome or superior mesenteric artery. Wilkie s syndrome or superior mesenteric artery syndrome is a rare aetiology of intestinal obstruction resulting from the compression of the third part of the duodenum between the superior mesenteric artery sma and the aorta 12. Superior mesenteric artery wilkies syndrome as a result.
This compression causes partial or complete blockage of the duodenum. It is a clinical entity characterized by compression of the third or transverse portion of the duodenum between the aorta and superior mesenteric artery sma. Wilkies syndrome, also commonly known as superior mesenteric artery. Prolonged gastroparesis after corrective surgery for wilkies.
Superior mesenteric artery sma syndrome known as wilkies syndrome is a rare cause of upper gastrointestinal obstruction. The purpose of this case report is to discuss the diagnosis and conservative management of a patient with both wilkie syndrome and nutcracker syndrome. Wilkie disease definition of wilkie disease by medical. Wilkie wilkinson 19032001, british auto mechanic and. Wilkie syndrome, also referred as superior mesenteric artery syndrome, is an unusual. Superior mesenteric artery wilkies syndrome as a result of. Fleming, thomas aloia, jeannicolas vauthey, claudius conrad background. Smas, also referred to as wilkie s syndrome, cast syndrome, aortomesenteric artery compression, etc. Superior mesenteric artery sma syndrome known as wilkies syndrome is a rare cause of.
Some studies report the incidence of superior mesenteric artery syndrome to be 0. She has tried proton pump inhibitors, glutenfree diet and lactosefree diet without any. After treatment the vomits and weight loss, to some extent, were. Conservative treatment was applied and the patient was discharged without.
This rare, potentially lifethreatening syndrome is typically caused by an angle of 625 between the aa and the sma, in comparison to the normal range of 3856, due to. Nov 05, 2019 smas, also referred to as wilkies syndrome, cast syndrome, aortomesenteric artery compression, etc. Wilkie s syndrome, well known as superior mesenteric artery syndrome, is a rare but wellrecognized clinical entity causing upper abdominal symptoms. Wilkies syndrome is a rare cause of duodenal obstruction that can easily be. Wilkies syndrome is an uncommon cause of upper small gut obstruction. Superior mesenteric artery syndrome is one of the rarest gastrointestinal disorders known to medical science. Functionally, the sma supplies the distal duodenum, twothirds of the transverse colon, and the. Superior mesenteric artery syndrome smas is a digestive condition that occurs when the duodenum the first part of the small intestine is compressed between two arteries the aorta and the superior mesenteric artery. Association of gastrointestinal motility disorders agmd association of gastrointestinal motility disorders agmd.
Wilkes stevenson syndrome symptoms, diagnosis, treatments. More detailed information about the symptoms, causes, and treatments of wilkes stevenson syndrome is available below symptoms of wilkes stevenson syndrome. This syndrome is a clinical phenomenon believed to be caused by compression of the third part of the duodenum between the sma and the aorta, leading to obstruction. Chronic vomiting and high ileus caused by intermittent duodenal compression between the aorta and superior mesenteric artery. The diagnostic challenges of identifying vascular constriction between the aorta and superior mesenteric artery have been answered by advances in the field of computed tomography. It is characterised by the compression of the duodenum in its third portion due to a narrowing of the space between the superior mesenteric artery and the aorta. A superior mesenteric artery syndrome smas was diagnosed in two young women with, respectively, a 2 and 1year history of postprandial vomiting and epigastric pain. Vascular compression of the duodenum, wilkie syndrome, cast syndrome, arteriomesenteric duodenal compression syndrome. Sma syndrome is estimated to have a mortality rate of 1 in 3. Wilkies syndrome is a rare disease that should be considered in the differential diagnosis of upper abdominal discomfort and weight loss. Loss of fatty tissue as a result of a variety of debilitating conditions is believed to be the etiologic factor causing the acute. It is caused by a narrowed aortomesenteric angle that leads to compression of the third portion of duodenum between the abdominal aorta aa and superior mesenteric artery sma.
Compression of the inferior part of the horizontal duodenum by the superior mesenteric artery may result in high intestinal obstruction with postprandial or positional discomfort, vomiting and weight loss. The syndrome is caused by compression of the third part of the duodenum in the angle between the aorta and the superior mesenteric artery. Semantic scholar extracted view of wilkies syndrome or superior mesenteric artery syndrome. Pdf superior mesenteric artery syndrome or wilkie syndrome. Superior mesenteric artery sma syndrome, also known as wilkies syndrome, is extremely rare and is characterized by postprandial epigastric pain, nausea, vomiting and. Patient with both wilkie syndrome and nutcracker syndrome. Wilkies syndrome or superior mesenteric artery syndrome is a rare aetiology of intestinal obstruction resulting from the compression of the third part of the duodenum between the superior mesenteric artery sma and the aorta 12. Superior mesenteric artery sma syndrome, also known as wilkie syndrome or cast syndrome or aortomesentric duodenal compression syndrome is a rare acquired vascular compression disorder in which acute angulation of the superior mesenteric artery sma results in compression of the third part of the duodenum, leading to obstruction. Smas, also referred to as wilkies syndrome, cast syndrome, aortomesenteric artery compression, etc.
Wilkies syndrome, also commonly known as superior mesenteric artery sma syndrome, is an infrequent and rare cause of small bowel obstruction. Aug 16, 2011 sma syndrome is also known as wilkies syndrome, cast syndrome, mesenteric root syndrome, chronic duodenal ileus and intermittent arteriomesenteric occlusion. Wilkies syndrome is an unusual cause of proximal intestinal obstruction. More detailed information about the symptoms, causes, and treatments of wilkes stevenson syndrome is available below. Wilkies syndrome, a rare cause of vomiting and weight. Wilkie syndrome definition of wilkie syndrome by medical.
Wilkies syndrome, a rare cause of intestinal obstruction, is related to anatomical and mechanical factors associated with the reduction of retroperitoneal fat padding. Smas occurs when the space between the superior mesenteric artery sma and the abdominal aorta narrows, resulting in compression of the duodenum. Laparoscopic strong procedure for wilkie syndrome complete intestinal derotation for sma syndrome lilian schwarz, jeffrey lee, matthew h. We report a case of yearold female who was diagnosed with sma syndrome. Superior mesenteric artery syndrome genetic and rare. It is caused by extrinsic compression of the duodenal segment of the intestine between the aorta and sma, causing significant postprandial abdominal pain and vomiting. Superior mesenteric artery sma syndrome, also known as wilkie syndrome or cast syndrome or aortomesentric duodenal compression syndrome is a rare acquired vascular compression disorder in which acute angulation of the superior mesenteric artery. Wilkes stevenson syndrome symptoms, diagnosis, treatments and. Superior mesenteric artery sma syndrome known as wilkie s syndrome is a rare cause of upper gastrointestinal obstruction. It is distinct from nutcracker syndrome, which is the entrapment of the left renal vein between the aa and the sma. Apr 20, 2018 metabolic syndrome, also called syndrome x, is a combination of conditions that raises your risk of diseases, such as type 2 diabetes, heart disease, and stroke. Tell a friend about us, add a link to this page, or visit the webmasters page for free fun content. Autopsy revealed a cachectic transgender woman with a grossly distended stomach and proximal duodenum containing 2 l of liquid.
Superior mesenteric artery sma syndrome is an uncommon but well recognized clinical entity characterized by compression of the third, or transverse, portion of the duodenum between the aorta and the superior mesenteric artery. Wilkies syndrome, a rare cause of vomiting and weight loss. Superior mesenteric artery sma syndrome, also called wilkie s syndrome or cast syndrome, is a rare disorder in which acute angulation of the sma causes compression of the third part of the duodenum between the sma and the aorta, leading to obstruction. Smas is caused by a compression of the inferior or third part of the duodenum resulting from the narrowing of the space between the superior mesenteric artery. Superior mesenteric artery sma syndrome, also known as wilkies syndrome and cast syndrome, is a rare gastrointestinal disease that leads to obstruction of the duodenum. Prolonged gastroparesis after corrective surgery for. Firstline treatment involves conservative management, but if. Wilkie artery the right colic artery when it occasionally crosses the duodenum. Metabolic syndrome, also called syndrome x, is a combination of conditions that raises your risk of diseases, such as type 2 diabetes, heart disease, and stroke. Superior mesenteric artery syndrome smas, also known as wilkies syndrome. Ultrasound imaging in diagnosis of superior mesenteric. Wilkie s syndrome is a rare disease that should be considered in the differential diagnosis of upper abdominal discomfort and weight loss. Acute dilatation of the stomachgastromesenteric ileus.
This is usually associated with conditions that cause significant weight loss, such as anorexia nervosa, malabsorption, or hypercatabolic states such as burns, major surgery, severe injuries, or malignancies. It is distinct from nutcracker syndrome, which is the entrapment of the left renal vein between the aa and the sma, although it is possible to be diagnosed with both conditions. Need awareness prevention research on superior mesenteric. Wilkie s syndrome is also known as superior mesenteric artery syndrome, cast syndrome, mesenteric root syndrome and chronic duodenal ileus 2. The patient continued to have normal renal function and she was managed conservatively. Wilkie rasmussen born 1958, cook islands politician and former cabinet minister. Wilkies syndrome is a rare cause of duodenal obstruction incidence. Wilkie s syndrome is a rare cause of duodenal obstruction incidence. We present one case of a 29yearold female with a recent history of. A 26yearold woman presented with recurrent upper abdominal pain, vomiting, loss of weight, early satiety, and fullness of upper abdomen for 2 years. Herein, we presented a patient with wilkie s syndrome and discussed the diagnostic difficulties and surgical treatment options. The findings in this patient with postprandial abdominal pain are suggestive of sma syndrome.
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